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Common Presentation of an Uncommon Disease: A Fatal Acute Aortic Dissection in a Young Male

Original article

Abstrak

Diseksi aorta jarang berlaku di kalangan kanak-kanak dan pemuda. Kami ingin membentangkan kes Diseksi Aorta Stanford B yang terjadi terhadap seorang pesakit lelaki berusia 30 tahun, yang telah membawa maut. Pesakit ini datang dengan aduan sakit perut akut yang teruk dan didapati bacaan tekanan darahnya tinggi. Walaupun tanpa tanda-tanda tipikal diseksi aorta, namun kadar kesakitannya yang teramat kuat disertai dengan tekanan darah yang amat tinggi menyebabkan kami mengesyaki diseksi aorta dalam kes ini. Abdomen ultrasound ada dilakukan di zon Kecemasan namun tanda khusus diseksi aorta iaitu “intimal flap” tidak dapat dikesan awal kerana bukan semua pegawai perubatan mahir dalam ultrasound. Dalam kes ini, komputer tomografi (CT) Abdomen dilakukan juga untuk membuktikan diagnosis ini. Walaubagaimanapun, keadaan klinikalnya semakin merosot dan pembedahan yang dilakukan tidak berjaya menyelamatkannya, lalu beliau meninggal dunia selepas 36 jam rawatan. Kami menekankan kepentingan untuk mengesyaki penyakit ini pada peringkat awal bersama bantuan kaedah ultrasonografi untuk mengesan ciri-cirinya dengan segera untuk membantu menangani penyakit yang serius ini. 

Abstract

Acute aortic dissection (AAD) is rare in the paediatric and young adult population. We present a fatal case of acute aortic dissection Stanford B in a young male diagnosed with hypertension. He presented with severe acute abdominal pain with malignant hypertension. He did not have any trauma to the chest or did not have history of an illicit drug abuse. He had no features suggestive of connective tissue disease as well as other typical signs of aortic dissection. The complain of acute, severe abdominal pain which was out of proportion and required multiple doses of intravenous opioid, raised the suspicion of aortic dissection in this case. Point of care sonography (POC) was done in Emergency Department (ED). However, due to its highly operator dependability, the intimal flap was missed. Computed tomography (CT) scan of abdomen was done and confirmed the diagnosis of AAD. Unfortunately, his clinical condition rapidly deteriorated few hours later with no response to surgical intervention and succumbed within 36 hours of admission. We highlighted the importance of the early recognition of this disease as well as the point of care sonography in ED as a diagnostic tool to tackle this time-sensitive disease.