Pleomorphic Adenoma Originating from Submandibular Salivary Gland in an 8-year-old Girl: A Case Report

Pleomorphic Adenoma Originating from Submandibular Salivary Gland
Vol. 2 No. 2 : 2007 (164-168)

Gani AN Gani AN
Megat Shiraz MAR Megat Shiraz MAR
Siti Aishah MA Siti Aishah MA
Norazizah M Norazizah M
Mazita A Mazita A
Sharifah NA Sharifah NA

Abstract
Pleomorphic adenoma (PA) typically presents as a benign slow growing, painless neoplasm of the parotid gland. PA arising from the submandibular gland in the paediatric age group is rare. Surgical excision is the treatment of choice. A case of PA in an 8-year-old Malay girl is presented. Clinically she presented with a painless right submandibular mass measuring 2x2cm. A diagnosis of Pleomorphic adenoma was made on Fine Needle Aspiration Cytology (FNAC). She underwent submandibulectomy uneventfully. Postoperatively after two years follow up, she is asymptomatic.
Keywords : pleomorphic adenoma, submandibular gland, submandibulectomy,
Abstrak
Adenoma pleomorfik (PA) ialah neoplasma epitelium kelenjar liur yang membesar perlahan-lahan dan biasanya didapati pada kelenjar liur parotid. Ia jarang didapati pada kelenjar liur submandibular terutama pada kumpulan umur pediatrik. Pembedahan adalah rawatan pilihan. Satu kes PA pada pesakit perempuan Melayu berumur 8 tahun dibentangkan. Pemeriksaan klinikal menunjukkan bengkakan di bahagian submandibular kanan berukuran 2x2sm. Diagnosis adenoma pleomorfik (PA) dibuat melalui sitologi sedutan jarum halus. Pesakit menjalani pembedahan submandibulektomi tanpa komplikasi. Dua tahun selepas pembedahan, pemeriksaan susulan menunjukkan pesakit masih asimptomatik.
Kata Kunci : Adenoma pleomorfik, kelenjar submandibular, submandibulektomi,

Correspondance Address
Dr Norhaslinda Abdul Gani , Department of Otorhinolaryngology, Faculty of Medicine, Universiti Kebangsaan Malaysia. Jalan Yaacob Latiff, Bandar Tun Razak, 56000 Cheras, Kuala Lumpur, Malaysia. Email: haslinda.gani@yahoo.com